Phenylketonuria: An Inborn Error of Phenylalanine Metabolism

Phenylketonuria (PKU) is an autosomal recessive inborn error of phenylalanine (Phe) metabolism resulting from deficiency of phenylalanine hydroxylase (PAH). Most forms of PKU and hyperphenylalaninaemia (HPA) are caused by mutations in the PAH gene on chromosome 12q23.2. Untreated PKU is associated w...

Full description

Bibliographic Details
Main Authors: Williams, R., Mamotte, Cyril, Burnett, J.
Format: Journal Article
Published: The Australasian Association of Clinical Biochemists Inc. 2008
Online Access:http://hdl.handle.net/20.500.11937/44157