ACTH therapy for West syndrome with severe hemophilia A

ACTH therapy for West syndrome with severe hemophilia A

Hemophilia A is an X-linked recessive disorder caused by factor VIII deficiency, which is an important factor in the coagulation system. Here, we describe a 1-year-old boy with hemophilia A who developed West syndrome (WS). Recombinant factor VIII was administered during adrenocorticotropic hormone...

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Main Authors: Kubota, Kazuo, Kinomura, Yoriko, Yamamoto, Takahiro, Ozeki, Michio, Kawamoto, Minako, Kawamoto, Norio, Fukao, Toshiyuki
Format: Online
Language:English
Published: Elsevier 2016
Online Access:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5118558/
id pubmed-5118558
recordtype oai_dc
spelling pubmed-51185582016-11-28 ACTH therapy for West syndrome with severe hemophilia A Kubota, Kazuo Kinomura, Yoriko Yamamoto, Takahiro Ozeki, Michio Kawamoto, Minako Kawamoto, Norio Fukao, Toshiyuki Case Report Hemophilia A is an X-linked recessive disorder caused by factor VIII deficiency, which is an important factor in the coagulation system. Here, we describe a 1-year-old boy with hemophilia A who developed West syndrome (WS). Recombinant factor VIII was administered during adrenocorticotropic hormone (ACTH) therapy to prevent intracranial hemorrhage. Infusion of factor VIII at fixed intervals is useful for the safe administration of ACTH therapy for patients with WS with severe hemophilia A. A coagulation screening test should be performed before ACTH therapy. Elsevier 2016-05-10 /pmc/articles/PMC5118558/ /pubmed/27896066 http://dx.doi.org/10.1016/j.ebcr.2016.04.007 Text en © 2016 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
repository_type Open Access Journal
institution_category Foreign Institution
institution US National Center for Biotechnology Information
building NCBI PubMed
collection Online Access
language English
format Online
author Kubota, Kazuo
Kinomura, Yoriko
Yamamoto, Takahiro
Ozeki, Michio
Kawamoto, Minako
Kawamoto, Norio
Fukao, Toshiyuki
spellingShingle Kubota, Kazuo
Kinomura, Yoriko
Yamamoto, Takahiro
Ozeki, Michio
Kawamoto, Minako
Kawamoto, Norio
Fukao, Toshiyuki
ACTH therapy for West syndrome with severe hemophilia A
author_facet Kubota, Kazuo
Kinomura, Yoriko
Yamamoto, Takahiro
Ozeki, Michio
Kawamoto, Minako
Kawamoto, Norio
Fukao, Toshiyuki
author_sort Kubota, Kazuo
title ACTH therapy for West syndrome with severe hemophilia A
title_short ACTH therapy for West syndrome with severe hemophilia A
title_full ACTH therapy for West syndrome with severe hemophilia A
title_fullStr ACTH therapy for West syndrome with severe hemophilia A
title_full_unstemmed ACTH therapy for West syndrome with severe hemophilia A
title_sort acth therapy for west syndrome with severe hemophilia a
description Hemophilia A is an X-linked recessive disorder caused by factor VIII deficiency, which is an important factor in the coagulation system. Here, we describe a 1-year-old boy with hemophilia A who developed West syndrome (WS). Recombinant factor VIII was administered during adrenocorticotropic hormone (ACTH) therapy to prevent intracranial hemorrhage. Infusion of factor VIII at fixed intervals is useful for the safe administration of ACTH therapy for patients with WS with severe hemophilia A. A coagulation screening test should be performed before ACTH therapy.
publisher Elsevier
publishDate 2016
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5118558/
_version_ 1613736153103466496

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