Giant Adrenal Cavernous Hemangioma in a Patient with Familial Adenomatous Polyposis

Adrenal hemangioma is an uncommon benign vascular tumor that is often discovered incidentally. It has never been reported in association with familial adenomatous polyposis. We report a case of a 60-year old man with a history of familial adenomatous polyposis, in whom a huge retroperitoneal cyst of...

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Bibliographic Details
Main Authors: Bacha, Dhouha, Chaabane, Abir, Khanche, Fatma, NĂ©chi, Saloua, Touinsi, Hassen, Chelbi, Emna
Format: Online
Language:English
Published: PAGEPress Publications, Pavia, Italy 2016
Online Access:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5067406/
Description
Summary:Adrenal hemangioma is an uncommon benign vascular tumor that is often discovered incidentally. It has never been reported in association with familial adenomatous polyposis. We report a case of a 60-year old man with a history of familial adenomatous polyposis, in whom a huge retroperitoneal cyst of 18x17 cm was discovered during routine radiologic evaluation. Because of the impossibility of ruling out the presence of malignancy, surgical cystectomy was performed, associated to a scheduled total colectomy. Pathological examination revealed that the cyst corresponded to an adrenal cavernous hemangioma. Colonic adenomas did not show signs of degeneration. Screening for adenomatous polyposis coli (APC) gene mutation was not carried out.