Young patient with generalized lymphangiomatosis: Differentiating the differential

We present the case of a 19-year-old man who was extensively evaluated in multiple centres for long-standing cough, dyspnea, and hemoptysis without a definitive diagnosis. His chest radiograph at presentation showed mediastinal widening, bilateral pleural effusions, and Kerley B lines. Computed tomo...

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Main Authors:	Putta, Tharani, Irodi, Aparna, Thangakunam, Balamugesh, Oliver, Ashwin, Gunasingam, Rajesh
Format:	Online
Language:	English
Published:	Medknow Publications & Media Pvt Ltd 2016
Online Access:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5036344/

id	pubmed-5036344
recordtype	oai_dc
spelling	pubmed-50363442016-11-17 Young patient with generalized lymphangiomatosis: Differentiating the differential Putta, Tharani Irodi, Aparna Thangakunam, Balamugesh Oliver, Ashwin Gunasingam, Rajesh Miscellaneous We present the case of a 19-year-old man who was extensively evaluated in multiple centres for long-standing cough, dyspnea, and hemoptysis without a definitive diagnosis. His chest radiograph at presentation showed mediastinal widening, bilateral pleural effusions, and Kerley B lines. Computed tomography of the thorax showed a confluent, fluid-density mediastinal lesion enveloping the mediastinal viscera without any mass effect. There were bilateral pleural effusions, prominent peribronchovascular interstitial thickening, interlobular septal thickening and lobular areas of ground glass density with relative sparing of apices. There were a few dilated retroperitoneal lymphatics and well-defined lytic lesions in the bones. In this case report, we aim to systematically discuss the relevant differentials and arrive at a diagnosis. We also briefly discuss the treatment options and prognosis along with our patient's course in the hospital and final outcome. Medknow Publications & Media Pvt Ltd 2016 /pmc/articles/PMC5036344/ /pubmed/27857472 http://dx.doi.org/10.4103/0971-3026.190416 Text en Copyright: © 2016 Indian Journal of Radiology and Imaging http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open access article distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 3.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as the author is credited and the new creations are licensed under the identical terms.
repository_type	Open Access Journal
institution_category	Foreign Institution
institution	US National Center for Biotechnology Information
building	NCBI PubMed
collection	Online Access
language	English
format	Online
author	Putta, Tharani Irodi, Aparna Thangakunam, Balamugesh Oliver, Ashwin Gunasingam, Rajesh
spellingShingle	Putta, Tharani Irodi, Aparna Thangakunam, Balamugesh Oliver, Ashwin Gunasingam, Rajesh Young patient with generalized lymphangiomatosis: Differentiating the differential
author_facet	Putta, Tharani Irodi, Aparna Thangakunam, Balamugesh Oliver, Ashwin Gunasingam, Rajesh
author_sort	Putta, Tharani
title	Young patient with generalized lymphangiomatosis: Differentiating the differential
title_short	Young patient with generalized lymphangiomatosis: Differentiating the differential
title_full	Young patient with generalized lymphangiomatosis: Differentiating the differential
title_fullStr	Young patient with generalized lymphangiomatosis: Differentiating the differential
title_full_unstemmed	Young patient with generalized lymphangiomatosis: Differentiating the differential
title_sort	young patient with generalized lymphangiomatosis: differentiating the differential
description	We present the case of a 19-year-old man who was extensively evaluated in multiple centres for long-standing cough, dyspnea, and hemoptysis without a definitive diagnosis. His chest radiograph at presentation showed mediastinal widening, bilateral pleural effusions, and Kerley B lines. Computed tomography of the thorax showed a confluent, fluid-density mediastinal lesion enveloping the mediastinal viscera without any mass effect. There were bilateral pleural effusions, prominent peribronchovascular interstitial thickening, interlobular septal thickening and lobular areas of ground glass density with relative sparing of apices. There were a few dilated retroperitoneal lymphatics and well-defined lytic lesions in the bones. In this case report, we aim to systematically discuss the relevant differentials and arrive at a diagnosis. We also briefly discuss the treatment options and prognosis along with our patient's course in the hospital and final outcome.
publisher	Medknow Publications & Media Pvt Ltd
publishDate	2016
url	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5036344/
_version_	1613660768524304384

Young patient with generalized lymphangiomatosis: Differentiating the differential

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