Initial Pulmonary Respiration Causes Massive Diaphragm Damage and Hyper-CKemia in Duchenne Muscular Dystrophy Dog

The molecular mechanism of muscle degeneration in a lethal muscle disorder Duchene muscular dystrophy (DMD) has not been fully elucidated. The dystrophic dog, a model of DMD, shows a high mortality rate with a marked increase in serum creatine kinase (CK) levels in the neonatal period. By measuring...

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Bibliographic Details
Main Authors: Nakamura, Akinori, Kobayashi, Masanori, Kuraoka, Mutsuki, Yuasa, Katsutoshi, Yugeta, Naoko, Okada, Takashi, Takeda, Shin'ichi
Format: Online
Language:English
Published: Nature Publishing Group 2013
Online Access:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3711052/