Malignant perivascular epithelioid cell tumor of the uterus

Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise speci...

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Main Authors: Bleeker, Jonathan S., Quevedo, J. Fernando, Folpe, Andrew L.
Format: Online
Language:English
Published: PAGEPress Publications 2012
Online Access:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3325741/
id pubmed-3325741
recordtype oai_dc
spelling pubmed-33257412012-04-24 Malignant perivascular epithelioid cell tumor of the uterus Bleeker, Jonathan S. Quevedo, J. Fernando Folpe, Andrew L. Case Report Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS), and one of the most common primary sites for PEComa-NOS is the uterus. The risk of aggressive behavior of these tumors has been linked to a number of factors evaluable on pathologic review following initial surgical resection. We report a case of PEComa-NOS of the uterus with multiple high-risk features, including frank vascular invasion, with no evidence of recurrent disease 18 months following initial surgical resection. PAGEPress Publications 2012-03-12 /pmc/articles/PMC3325741/ /pubmed/22532912 http://dx.doi.org/10.4081/rt.2012.e14 Text en ©Copyright J.S. Bleeker et al., 2012 This work is licensed under a Creative Commons Attribution NonCommercial 3.0 License (CC BY-NC 3.0). Licensee PAGEPress, Italy
repository_type Open Access Journal
institution_category Foreign Institution
institution US National Center for Biotechnology Information
building NCBI PubMed
collection Online Access
language English
format Online
author Bleeker, Jonathan S.
Quevedo, J. Fernando
Folpe, Andrew L.
spellingShingle Bleeker, Jonathan S.
Quevedo, J. Fernando
Folpe, Andrew L.
Malignant perivascular epithelioid cell tumor of the uterus
author_facet Bleeker, Jonathan S.
Quevedo, J. Fernando
Folpe, Andrew L.
author_sort Bleeker, Jonathan S.
title Malignant perivascular epithelioid cell tumor of the uterus
title_short Malignant perivascular epithelioid cell tumor of the uterus
title_full Malignant perivascular epithelioid cell tumor of the uterus
title_fullStr Malignant perivascular epithelioid cell tumor of the uterus
title_full_unstemmed Malignant perivascular epithelioid cell tumor of the uterus
title_sort malignant perivascular epithelioid cell tumor of the uterus
description Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non-classic anatomic distributions are known as perivascular epithelioid cell tumor-not otherwise specified (PEComa-NOS), and one of the most common primary sites for PEComa-NOS is the uterus. The risk of aggressive behavior of these tumors has been linked to a number of factors evaluable on pathologic review following initial surgical resection. We report a case of PEComa-NOS of the uterus with multiple high-risk features, including frank vascular invasion, with no evidence of recurrent disease 18 months following initial surgical resection.
publisher PAGEPress Publications
publishDate 2012
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3325741/
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