Primary Malignant Fibrous Histiocytoma: A Rare Case
Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was...
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2011
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pubmed-31991082011-10-25 Primary Malignant Fibrous Histiocytoma: A Rare Case Katsourakis, Anastasios Noussios, George Hadjis, Iosif Evangelou, Neofitos Chatzitheoklitos, Efthimios Case Report Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was found. The patient underwent complete surgical removal of the tumor. A diagnosis of MFN (undifferentiated high-grade pleomorphic sarcoma) was made. The patient received adjuvant chemotherapy with Gemcitabine. Two years after the operation, the patient died due to recurrence of the disease. MFH of the small intestine is an extremely rare neoplasm with an aggressive biological behaviour. In this paper, pathogenesis, natural history, and treatment are reviewed. Hindawi Publishing Corporation 2011 2011-10-18 /pmc/articles/PMC3199108/ /pubmed/22028720 http://dx.doi.org/10.1155/2011/134801 Text en Copyright © 2011 Anastasios Katsourakis et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
repository_type |
Open Access Journal |
institution_category |
Foreign Institution |
institution |
US National Center for Biotechnology Information |
building |
NCBI PubMed |
collection |
Online Access |
language |
English |
format |
Online |
author |
Katsourakis, Anastasios Noussios, George Hadjis, Iosif Evangelou, Neofitos Chatzitheoklitos, Efthimios |
spellingShingle |
Katsourakis, Anastasios Noussios, George Hadjis, Iosif Evangelou, Neofitos Chatzitheoklitos, Efthimios Primary Malignant Fibrous Histiocytoma: A Rare Case |
author_facet |
Katsourakis, Anastasios Noussios, George Hadjis, Iosif Evangelou, Neofitos Chatzitheoklitos, Efthimios |
author_sort |
Katsourakis, Anastasios |
title |
Primary Malignant Fibrous Histiocytoma: A Rare Case |
title_short |
Primary Malignant Fibrous Histiocytoma: A Rare Case |
title_full |
Primary Malignant Fibrous Histiocytoma: A Rare Case |
title_fullStr |
Primary Malignant Fibrous Histiocytoma: A Rare Case |
title_full_unstemmed |
Primary Malignant Fibrous Histiocytoma: A Rare Case |
title_sort |
primary malignant fibrous histiocytoma: a rare case |
description |
Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was found. The patient underwent complete surgical removal of the tumor. A diagnosis of MFN (undifferentiated high-grade pleomorphic sarcoma) was made. The patient received adjuvant chemotherapy with Gemcitabine. Two years after the operation, the patient died due to recurrence of the disease. MFH of the small intestine is an extremely rare neoplasm with an aggressive biological behaviour. In this paper, pathogenesis, natural history, and treatment are reviewed. |
publisher |
Hindawi Publishing Corporation |
publishDate |
2011 |
url |
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3199108/ |
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1611482727508344832 |