Primary Malignant Fibrous Histiocytoma: A Rare Case

Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was...

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Main Authors: Katsourakis, Anastasios, Noussios, George, Hadjis, Iosif, Evangelou, Neofitos, Chatzitheoklitos, Efthimios
Format: Online
Language:English
Published: Hindawi Publishing Corporation 2011
Online Access:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3199108/
id pubmed-3199108
recordtype oai_dc
spelling pubmed-31991082011-10-25 Primary Malignant Fibrous Histiocytoma: A Rare Case Katsourakis, Anastasios Noussios, George Hadjis, Iosif Evangelou, Neofitos Chatzitheoklitos, Efthimios Case Report Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was found. The patient underwent complete surgical removal of the tumor. A diagnosis of MFN (undifferentiated high-grade pleomorphic sarcoma) was made. The patient received adjuvant chemotherapy with Gemcitabine. Two years after the operation, the patient died due to recurrence of the disease. MFH of the small intestine is an extremely rare neoplasm with an aggressive biological behaviour. In this paper, pathogenesis, natural history, and treatment are reviewed. Hindawi Publishing Corporation 2011 2011-10-18 /pmc/articles/PMC3199108/ /pubmed/22028720 http://dx.doi.org/10.1155/2011/134801 Text en Copyright © 2011 Anastasios Katsourakis et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
repository_type Open Access Journal
institution_category Foreign Institution
institution US National Center for Biotechnology Information
building NCBI PubMed
collection Online Access
language English
format Online
author Katsourakis, Anastasios
Noussios, George
Hadjis, Iosif
Evangelou, Neofitos
Chatzitheoklitos, Efthimios
spellingShingle Katsourakis, Anastasios
Noussios, George
Hadjis, Iosif
Evangelou, Neofitos
Chatzitheoklitos, Efthimios
Primary Malignant Fibrous Histiocytoma: A Rare Case
author_facet Katsourakis, Anastasios
Noussios, George
Hadjis, Iosif
Evangelou, Neofitos
Chatzitheoklitos, Efthimios
author_sort Katsourakis, Anastasios
title Primary Malignant Fibrous Histiocytoma: A Rare Case
title_short Primary Malignant Fibrous Histiocytoma: A Rare Case
title_full Primary Malignant Fibrous Histiocytoma: A Rare Case
title_fullStr Primary Malignant Fibrous Histiocytoma: A Rare Case
title_full_unstemmed Primary Malignant Fibrous Histiocytoma: A Rare Case
title_sort primary malignant fibrous histiocytoma: a rare case
description Malignant fibrous histiocytoma (MFH) of the small intestine is an extremely rare condition. It occurs most commonly in the extremities and the trunk. We report a case of a 67-year-old woman who admitted with fever, myalgia, and altered status. After thorough investigation, a tumor of the jejunum was found. The patient underwent complete surgical removal of the tumor. A diagnosis of MFN (undifferentiated high-grade pleomorphic sarcoma) was made. The patient received adjuvant chemotherapy with Gemcitabine. Two years after the operation, the patient died due to recurrence of the disease. MFH of the small intestine is an extremely rare neoplasm with an aggressive biological behaviour. In this paper, pathogenesis, natural history, and treatment are reviewed.
publisher Hindawi Publishing Corporation
publishDate 2011
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3199108/
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