Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding

Although mild increase in pulmonary vascular resistance following intracardiac repair of tetralogy of Fallot is often seen in the early postoperative period, it usually subsides without any sequel. Persistent severe pulmonary artery hypertension after total correction is rare. We report a child with...

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Main Authors:	Kumar, Bhupesh, Puri, Goverdhan D., Manoj, Rohit, Gupta, Kirti, Shyam, K. S.
Format:	Online
Language:	English
Published:	Medknow Publications 2011
Online Access:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3198627/

id	pubmed-3198627
recordtype	oai_dc
spelling	pubmed-31986272011-10-27 Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding Kumar, Bhupesh Puri, Goverdhan D. Manoj, Rohit Gupta, Kirti Shyam, K. S. Case Report Although mild increase in pulmonary vascular resistance following intracardiac repair of tetralogy of Fallot is often seen in the early postoperative period, it usually subsides without any sequel. Persistent severe pulmonary artery hypertension after total correction is rare. We report a child with tetralogy of Fallot and Down's syndrome, who developed severe pulmonary hypertension and low cardiac output syndrome following an intracardiac repair, which was resistant to specific pulmonary vasodilators and increasing ionotropes. The post correction echocardiogram suggested an intact ventricular septal defect patch, no residual gradient across the right ventricular outflow tract, with free pulmonary regurgitation. The child had a poor outcome. A postmortem biopsy revealed histopathological signs of pulmonary hypertension. Medknow Publications 2011 /pmc/articles/PMC3198627/ /pubmed/22034598 http://dx.doi.org/10.4103/2045-8932.78099 Text en Copyright: © Pulmonary Circulation http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
repository_type	Open Access Journal
institution_category	Foreign Institution
institution	US National Center for Biotechnology Information
building	NCBI PubMed
collection	Online Access
language	English
format	Online
author	Kumar, Bhupesh Puri, Goverdhan D. Manoj, Rohit Gupta, Kirti Shyam, K. S.
spellingShingle	Kumar, Bhupesh Puri, Goverdhan D. Manoj, Rohit Gupta, Kirti Shyam, K. S. Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding
author_facet	Kumar, Bhupesh Puri, Goverdhan D. Manoj, Rohit Gupta, Kirti Shyam, K. S.
author_sort	Kumar, Bhupesh
title	Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding
title_short	Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding
title_full	Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding
title_fullStr	Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding
title_full_unstemmed	Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding
title_sort	severe pulmonary artery hypertension following intracardiac repair of tetralogy of fallot: an unusual finding
description	Although mild increase in pulmonary vascular resistance following intracardiac repair of tetralogy of Fallot is often seen in the early postoperative period, it usually subsides without any sequel. Persistent severe pulmonary artery hypertension after total correction is rare. We report a child with tetralogy of Fallot and Down's syndrome, who developed severe pulmonary hypertension and low cardiac output syndrome following an intracardiac repair, which was resistant to specific pulmonary vasodilators and increasing ionotropes. The post correction echocardiogram suggested an intact ventricular septal defect patch, no residual gradient across the right ventricular outflow tract, with free pulmonary regurgitation. The child had a poor outcome. A postmortem biopsy revealed histopathological signs of pulmonary hypertension.
publisher	Medknow Publications
publishDate	2011
url	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3198627/
_version_	1611482540077481984

Severe pulmonary artery hypertension following intracardiac repair of tetralogy of Fallot: An unusual finding

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