Mesenteric fibromatosis: a little known and rare aggressive benign tumor
Mesenteric fibromatosis or desmoid tumor, is a rare benign tumor originating from fibrous tissue proliferation, commonly affecting young adults. Clinical presentations vary widely, often manifesting with abdominal symptoms. Here, we describe a 34-year-old man presenting with peritonism symptoms, inc...
| Main Authors: | , |
|---|---|
| Format: | Conference or Workshop Item |
| Language: | English |
| Published: |
Malaysian Congress of Radiology 2024
2024
|
| Online Access: | http://psasir.upm.edu.my/id/eprint/121228/ http://psasir.upm.edu.my/id/eprint/121228/1/121228.pdf |
| Summary: | Mesenteric fibromatosis or desmoid tumor, is a rare benign tumor originating from fibrous tissue proliferation, commonly affecting young adults. Clinical presentations vary widely, often manifesting with abdominal symptoms. Here, we describe a 34-year-old man presenting with peritonism symptoms, incidentally, discovered to have a mesenteric mass on contrasted CT Abdomen. Surgical exploration unveiled extensive involvement, posing a risk of bowel ischemia, prompting biopsy for confirmation. Subsequent CT scans revealed postoperative complications, including a necrotic ruptured mass and intraabdominal collections, managed with drainage and antibiotics. Despite risks, surgical resection remained the primary treatment, albeit with potential complications due to the mass's proximity to the Superior Mesenteric Artery. Radiotherapy or chemotherapy were not suitable due to slow tumor growth. While mesenteric angiography with angioembolization was offered as an alternative, the patient opted for surveillance through repeated imaging. This case highlights the diverse clinical features, its potential complications and available management options. |
|---|