Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications

Lymphatic malformation (LM) is a dysfunction of the lymphatic system that is associated with genetic diseases. The clinical manifestation is established, but the outcome concerning genetic abnormalities is still not well understood. This review reports the advancement of technology in detecting LM a...

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Main Authors: Mohd Nor, Nurul Huda, Mohd Nor, Khadijah, Maniam, Sandra, Hod, Rafidah
Format: Article
Language:English
Published: Universiti Malaya 2024
Online Access:http://psasir.upm.edu.my/id/eprint/119856/
http://psasir.upm.edu.my/id/eprint/119856/1/119856.pdf
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author Mohd Nor, Nurul Huda
Mohd Nor, Khadijah
Maniam, Sandra
Hod, Rafidah
author_facet Mohd Nor, Nurul Huda
Mohd Nor, Khadijah
Maniam, Sandra
Hod, Rafidah
author_sort Mohd Nor, Nurul Huda
building UPM Institutional Repository
collection Online Access
description Lymphatic malformation (LM) is a dysfunction of the lymphatic system that is associated with genetic diseases. The clinical manifestation is established, but the outcome concerning genetic abnormalities is still not well understood. This review reports the advancement of technology in detecting LM antenatally, its associated genetic factors, and the complications of LM. Articles which were mainly case reports published from 1983 to 2023 were obtained from the search in Ovid MEDLINE and Scopus using the keywords “gene*”, OR, “DNA”, OR “epigenetic*” AND “lymphatic malformation” OR “cystic hygroma”. The advancement of technology over the years has contributed to the various types of genetic investigations conducted on a foetus with LM, including fluorescence in situ hybridization and multiplex ligation-dependent probe amplification. Poor prognosis indicated by the presence of genetic or karyotype abnormality results in opted termination of pregnancy, intrauterine death, or death at early hours of life. The PTPNII, FOXC2, FOXF1, and SRY genes and various chromosome abnormalities are associated with LM. The complications of LM include bone deformity, cardiac and urinary anomalies, and the worst is foetal hydrops. This critical dysfunction warrants future research directions to identify risk factors or biomarkers to prevent future cases of pregnancy with LM.
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spelling upm-1198562025-09-11T04:16:45Z http://psasir.upm.edu.my/id/eprint/119856/ Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications Mohd Nor, Nurul Huda Mohd Nor, Khadijah Maniam, Sandra Hod, Rafidah Lymphatic malformation (LM) is a dysfunction of the lymphatic system that is associated with genetic diseases. The clinical manifestation is established, but the outcome concerning genetic abnormalities is still not well understood. This review reports the advancement of technology in detecting LM antenatally, its associated genetic factors, and the complications of LM. Articles which were mainly case reports published from 1983 to 2023 were obtained from the search in Ovid MEDLINE and Scopus using the keywords “gene*”, OR, “DNA”, OR “epigenetic*” AND “lymphatic malformation” OR “cystic hygroma”. The advancement of technology over the years has contributed to the various types of genetic investigations conducted on a foetus with LM, including fluorescence in situ hybridization and multiplex ligation-dependent probe amplification. Poor prognosis indicated by the presence of genetic or karyotype abnormality results in opted termination of pregnancy, intrauterine death, or death at early hours of life. The PTPNII, FOXC2, FOXF1, and SRY genes and various chromosome abnormalities are associated with LM. The complications of LM include bone deformity, cardiac and urinary anomalies, and the worst is foetal hydrops. This critical dysfunction warrants future research directions to identify risk factors or biomarkers to prevent future cases of pregnancy with LM. Universiti Malaya 2024 Article PeerReviewed text en http://psasir.upm.edu.my/id/eprint/119856/1/119856.pdf Mohd Nor, Nurul Huda and Mohd Nor, Khadijah and Maniam, Sandra and Hod, Rafidah (2024) Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications. Journal of Health and Translational Medicine, 27 (2). pp. 93-101. ISSN 1823-7339; eISSN: 2289-392X https://jummec.um.edu.my/index.php/jummec/issue/view/2330
spellingShingle Mohd Nor, Nurul Huda
Mohd Nor, Khadijah
Maniam, Sandra
Hod, Rafidah
Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
title Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
title_full Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
title_fullStr Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
title_full_unstemmed Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
title_short Overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
title_sort overview of the antenatal detection of lymphatic malformation, its associated genetic factors, and the complications
url http://psasir.upm.edu.my/id/eprint/119856/
http://psasir.upm.edu.my/id/eprint/119856/
http://psasir.upm.edu.my/id/eprint/119856/1/119856.pdf