A rare presentation of plexiform neurofibroma
We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerize...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
Pusat Perubatan Universiti Kebangsaan Malaysia
2018
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| Online Access: | http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/1/8._poh__syed.pdf |
| _version_ | 1848813034348216320 |
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| author | Poh, Khay Wei Syed Osman SIH, |
| author_facet | Poh, Khay Wei Syed Osman SIH, |
| author_sort | Poh, Khay Wei |
| building | UKM Institutional Repository |
| collection | Online Access |
| description | We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform neurofibroma of the lacrimal gland. Further physical examination confirmed presence of multiple café-au-lait spots. He was diagnosed as Neurofibromatosis Type 1. |
| first_indexed | 2025-11-15T00:11:46Z |
| format | Article |
| id | oai:generic.eprints.org:12556 |
| institution | Universiti Kebangasaan Malaysia |
| institution_category | Local University |
| language | English |
| last_indexed | 2025-11-15T00:11:46Z |
| publishDate | 2018 |
| publisher | Pusat Perubatan Universiti Kebangsaan Malaysia |
| recordtype | eprints |
| repository_type | Digital Repository |
| spelling | oai:generic.eprints.org:125562019-02-14T21:33:41Z http://journalarticle.ukm.my/12556/ A rare presentation of plexiform neurofibroma Poh, Khay Wei Syed Osman SIH, We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform neurofibroma of the lacrimal gland. Further physical examination confirmed presence of multiple café-au-lait spots. He was diagnosed as Neurofibromatosis Type 1. Pusat Perubatan Universiti Kebangsaan Malaysia 2018 Article PeerReviewed application/pdf en http://journalarticle.ukm.my/12556/1/8._poh__syed.pdf Poh, Khay Wei and Syed Osman SIH, (2018) A rare presentation of plexiform neurofibroma. Journal of Surgical Academia, 8 (1). pp. 39-42. ISSN 2231-7481 http://jsurgacad.com/toc/8/1 |
| spellingShingle | Poh, Khay Wei Syed Osman SIH, A rare presentation of plexiform neurofibroma |
| title | A rare presentation of plexiform neurofibroma |
| title_full | A rare presentation of plexiform neurofibroma |
| title_fullStr | A rare presentation of plexiform neurofibroma |
| title_full_unstemmed | A rare presentation of plexiform neurofibroma |
| title_short | A rare presentation of plexiform neurofibroma |
| title_sort | rare presentation of plexiform neurofibroma |
| url | http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/1/8._poh__syed.pdf |