Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease

Single nucleotide variants (SNVs) within and surrounding the complement receptor 1 (CR1) gene show some of the strongest genome-wide association signals with late-onset Alzheimer’s disease. Some studies have suggested that this association signal is due to a duplication allele (CR1-B) of a low copy...

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Main Authors: Kucukkilic, Ezgi, Brookes, Keeley, Barber, Imelda, Guetta-Baranes, Tamar, Morgan, Kevin, Hollox, Edward
Format: Article
Language:English
English
Published: Springer 2018
Online Access:https://eprints.nottingham.ac.uk/50597/
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author Kucukkilic, Ezgi
Brookes, Keeley
Barber, Imelda
Guetta-Baranes, Tamar
Morgan, Kevin
Hollox, Edward
author_facet Kucukkilic, Ezgi
Brookes, Keeley
Barber, Imelda
Guetta-Baranes, Tamar
Morgan, Kevin
Hollox, Edward
author_sort Kucukkilic, Ezgi
building Nottingham Research Data Repository
collection Online Access
description Single nucleotide variants (SNVs) within and surrounding the complement receptor 1 (CR1) gene show some of the strongest genome-wide association signals with late-onset Alzheimer’s disease. Some studies have suggested that this association signal is due to a duplication allele (CR1-B) of a low copy repeat (LCR) within the CR1 gene, which increases the number of complement C3b/C4b-binding sites in the mature receptor. In this study, we develop a triplex paralogue ratio test (PRT) assay for CR1 LCR copy number allowing large numbers of samples to be typed with a limited amount of DNA. We also develop a CR1-B allele-specific PCR based on the junction generated by an historical non-allelic homologous recombination event between CR1 LCRs. We use these methods to genotype CR1 and measure CR1-B allele frequency in both late-onset and early-onset cases and unaffected controls from the United Kingdom. Our data support an association of late-onset Alzheimer’s disease with the CR1-B allele, and confirm that this allele occurs most frequently on the risk haplotype defined by SNV alleles. Furthermore, regression models incorporating CR1-B genotype provide a bitter fit to our data compared to incorporating the SNP-defined risk haplotype, supporting the CR1-B allele as the variant underlying the increased risk of late-onset Alzheimer’s disease.
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spelling nottingham-505972018-06-12T05:55:00Z https://eprints.nottingham.ac.uk/50597/ Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease Kucukkilic, Ezgi Brookes, Keeley Barber, Imelda Guetta-Baranes, Tamar Morgan, Kevin Hollox, Edward Single nucleotide variants (SNVs) within and surrounding the complement receptor 1 (CR1) gene show some of the strongest genome-wide association signals with late-onset Alzheimer’s disease. Some studies have suggested that this association signal is due to a duplication allele (CR1-B) of a low copy repeat (LCR) within the CR1 gene, which increases the number of complement C3b/C4b-binding sites in the mature receptor. In this study, we develop a triplex paralogue ratio test (PRT) assay for CR1 LCR copy number allowing large numbers of samples to be typed with a limited amount of DNA. We also develop a CR1-B allele-specific PCR based on the junction generated by an historical non-allelic homologous recombination event between CR1 LCRs. We use these methods to genotype CR1 and measure CR1-B allele frequency in both late-onset and early-onset cases and unaffected controls from the United Kingdom. Our data support an association of late-onset Alzheimer’s disease with the CR1-B allele, and confirm that this allele occurs most frequently on the risk haplotype defined by SNV alleles. Furthermore, regression models incorporating CR1-B genotype provide a bitter fit to our data compared to incorporating the SNP-defined risk haplotype, supporting the CR1-B allele as the variant underlying the increased risk of late-onset Alzheimer’s disease. Springer 2018-04-19 Article PeerReviewed application/pdf en cc_by https://eprints.nottingham.ac.uk/50597/8/10.1007%252Fs00439-018-1883-2.pdf application/pdf en cc_by https://eprints.nottingham.ac.uk/50597/1/284711.full.pdf Kucukkilic, Ezgi, Brookes, Keeley, Barber, Imelda, Guetta-Baranes, Tamar, Morgan, Kevin and Hollox, Edward (2018) Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease. Human Genetics . pp. 1-10. ISSN 1432-1203 https://link.springer.com/article/10.1007%2Fs00439-018-1883-2 doi:10.1007/s00439-018-1883-2 doi:10.1007/s00439-018-1883-2
spellingShingle Kucukkilic, Ezgi
Brookes, Keeley
Barber, Imelda
Guetta-Baranes, Tamar
Morgan, Kevin
Hollox, Edward
Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
title Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
title_full Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
title_fullStr Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
title_full_unstemmed Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
title_short Complement receptor 1 gene (CR1) intragenic duplication and risk of Alzheimer’s disease
title_sort complement receptor 1 gene (cr1) intragenic duplication and risk of alzheimer’s disease
url https://eprints.nottingham.ac.uk/50597/
https://eprints.nottingham.ac.uk/50597/
https://eprints.nottingham.ac.uk/50597/