Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array

We have screened sporadic early-onset Alzheimer’s disease (sEOAD, n=408) samples using the NeuroX array for known causative and predicted pathogenic variants in 16 genes linked to familial forms of neurodegeneration. We found two sEOAD individuals harbouring a known causative variant in PARK2 known...

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Main Authors: Barber, Imelda S., Braae, Anne, Clement, Naomi, Patel, Tulsi, Guetta-Baranes, Tamar, Brookes, Keeley, Medway, Christopher, Chappell, Sally, Guerreiro, Rita, Bras, Jose, Hernandez, Dena, Singleton, Andrew, Hardy, John, Mann, David M., Morgan, Kevin
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Published: Elsevier 2017
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Online Access:https://eprints.nottingham.ac.uk/36987/
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author Barber, Imelda S.
Braae, Anne
Clement, Naomi
Patel, Tulsi
Guetta-Baranes, Tamar
Brookes, Keeley
Medway, Christopher
Chappell, Sally
Guerreiro, Rita
Bras, Jose
Hernandez, Dena
Singleton, Andrew
Hardy, John
Mann, David M.
Morgan, Kevin
author_facet Barber, Imelda S.
Braae, Anne
Clement, Naomi
Patel, Tulsi
Guetta-Baranes, Tamar
Brookes, Keeley
Medway, Christopher
Chappell, Sally
Guerreiro, Rita
Bras, Jose
Hernandez, Dena
Singleton, Andrew
Hardy, John
Mann, David M.
Morgan, Kevin
author_sort Barber, Imelda S.
building Nottingham Research Data Repository
collection Online Access
description We have screened sporadic early-onset Alzheimer’s disease (sEOAD, n=408) samples using the NeuroX array for known causative and predicted pathogenic variants in 16 genes linked to familial forms of neurodegeneration. We found two sEOAD individuals harbouring a known causative variant in PARK2 known to cause early-onset Parkinson’s disease (EOPD); p.T240M (n=1) and p.Q34fs delAG (n=1). Additionally, we identified three sEOAD individuals harbouring a predicted pathogenic variant in MAPT (p.A469T) which has previously been associated with AD. It is currently unknown if these variants affect susceptibility to sEOAD, further studies would be needed to establish this. This work highlights the need to screen sEOAD individuals for variants that are more classically attributed to other forms of neurodegeneration.
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publishDate 2017
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spelling nottingham-369872020-05-04T18:28:47Z https://eprints.nottingham.ac.uk/36987/ Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array Barber, Imelda S. Braae, Anne Clement, Naomi Patel, Tulsi Guetta-Baranes, Tamar Brookes, Keeley Medway, Christopher Chappell, Sally Guerreiro, Rita Bras, Jose Hernandez, Dena Singleton, Andrew Hardy, John Mann, David M. Morgan, Kevin We have screened sporadic early-onset Alzheimer’s disease (sEOAD, n=408) samples using the NeuroX array for known causative and predicted pathogenic variants in 16 genes linked to familial forms of neurodegeneration. We found two sEOAD individuals harbouring a known causative variant in PARK2 known to cause early-onset Parkinson’s disease (EOPD); p.T240M (n=1) and p.Q34fs delAG (n=1). Additionally, we identified three sEOAD individuals harbouring a predicted pathogenic variant in MAPT (p.A469T) which has previously been associated with AD. It is currently unknown if these variants affect susceptibility to sEOAD, further studies would be needed to establish this. This work highlights the need to screen sEOAD individuals for variants that are more classically attributed to other forms of neurodegeneration. Elsevier 2017-01-31 Article PeerReviewed Barber, Imelda S., Braae, Anne, Clement, Naomi, Patel, Tulsi, Guetta-Baranes, Tamar, Brookes, Keeley, Medway, Christopher, Chappell, Sally, Guerreiro, Rita, Bras, Jose, Hernandez, Dena, Singleton, Andrew, Hardy, John, Mann, David M. and Morgan, Kevin (2017) Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array. Neurobiology of Aging, 49 . 215.e1-215.e8. ISSN 1558-1497 Alzheimer's Disease Parkinson's Disease Sporadic Early-onset NeuroX Screening http://www.sciencedirect.com/science/article/pii/S0197458016302214 doi:10.1016/j.neurobiolaging.2016.09.008 doi:10.1016/j.neurobiolaging.2016.09.008
spellingShingle Alzheimer's Disease
Parkinson's Disease
Sporadic
Early-onset
NeuroX
Screening
Barber, Imelda S.
Braae, Anne
Clement, Naomi
Patel, Tulsi
Guetta-Baranes, Tamar
Brookes, Keeley
Medway, Christopher
Chappell, Sally
Guerreiro, Rita
Bras, Jose
Hernandez, Dena
Singleton, Andrew
Hardy, John
Mann, David M.
Morgan, Kevin
Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array
title Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array
title_full Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array
title_fullStr Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array
title_full_unstemmed Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array
title_short Mutation analysis of sporadic early-onset Alzheimer's disease using the NeuroX array
title_sort mutation analysis of sporadic early-onset alzheimer's disease using the neurox array
topic Alzheimer's Disease
Parkinson's Disease
Sporadic
Early-onset
NeuroX
Screening
url https://eprints.nottingham.ac.uk/36987/
https://eprints.nottingham.ac.uk/36987/
https://eprints.nottingham.ac.uk/36987/