Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study

Background: It is unclear why cystic fibrosis (CF) survival has improved. We wished to quantify increases in CF median age of death in the context of general population survival improvement. Method: Death registration data analysis (US, England & Wales (E&W)—1972–2009). Results: CF median...

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Main Authors: Hurley, Matthew, McKeeve, Tricia M., Prayle, Andrew P., Smyth, Alan R., Fogarty, Andrew W.
Format: Article
Published: Elsevier 2014
Subjects:
Online Access:https://eprints.nottingham.ac.uk/31674/
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author Hurley, Matthew
McKeeve, Tricia M.
Prayle, Andrew P.
Smyth, Alan R.
Fogarty, Andrew W.
author_facet Hurley, Matthew
McKeeve, Tricia M.
Prayle, Andrew P.
Smyth, Alan R.
Fogarty, Andrew W.
author_sort Hurley, Matthew
building Nottingham Research Data Repository
collection Online Access
description Background: It is unclear why cystic fibrosis (CF) survival has improved. We wished to quantify increases in CF median age of death in the context of general population survival improvement. Method: Death registration data analysis (US, England & Wales (E&W)—1972–2009). Results: CF median age of death is higher in US than E&W and greater for males, opposite to that of death from all causes. CF median age of death has increased by 0.543 life years per year (E&W, US combined (95% confidence interval 0.506, 0.582)). The difference in median age at death between those dying from all causes and CF decreased in both territories. CF median age of death for males is greater than for females in both territories. This gap has not narrowed. Conclusion: The median age of death of people with CF is improving more rapidly than that of the general population in US and E&W.
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spelling nottingham-316742020-05-04T16:48:38Z https://eprints.nottingham.ac.uk/31674/ Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study Hurley, Matthew McKeeve, Tricia M. Prayle, Andrew P. Smyth, Alan R. Fogarty, Andrew W. Background: It is unclear why cystic fibrosis (CF) survival has improved. We wished to quantify increases in CF median age of death in the context of general population survival improvement. Method: Death registration data analysis (US, England & Wales (E&W)—1972–2009). Results: CF median age of death is higher in US than E&W and greater for males, opposite to that of death from all causes. CF median age of death has increased by 0.543 life years per year (E&W, US combined (95% confidence interval 0.506, 0.582)). The difference in median age at death between those dying from all causes and CF decreased in both territories. CF median age of death for males is greater than for females in both territories. This gap has not narrowed. Conclusion: The median age of death of people with CF is improving more rapidly than that of the general population in US and E&W. Elsevier 2014-07-01 Article PeerReviewed Hurley, Matthew, McKeeve, Tricia M., Prayle, Andrew P., Smyth, Alan R. and Fogarty, Andrew W. (2014) Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study. Journal of Cystic Fibrosis, 13 (4). pp. 410-415. ISSN 1873-5010 Cystic fibrosis; Survival; Mortality; Healthcare http://www.sciencedirect.com/science/article/pii/S1569199313002270 doi:10.1016/j.jcf.2013.12.002 doi:10.1016/j.jcf.2013.12.002
spellingShingle Cystic fibrosis; Survival; Mortality; Healthcare
Hurley, Matthew
McKeeve, Tricia M.
Prayle, Andrew P.
Smyth, Alan R.
Fogarty, Andrew W.
Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study
title Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study
title_full Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study
title_fullStr Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study
title_full_unstemmed Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study
title_short Rate of improvement of CF life expectancy exceeds that of general population: observational death registration study
title_sort rate of improvement of cf life expectancy exceeds that of general population: observational death registration study
topic Cystic fibrosis; Survival; Mortality; Healthcare
url https://eprints.nottingham.ac.uk/31674/
https://eprints.nottingham.ac.uk/31674/
https://eprints.nottingham.ac.uk/31674/