A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach
Prader-Willi Syndrome (PWS) is a genetically determined neurodevelopmental disorder occurring in 1 in 15,000 births. PWS is a rare case in Malaysia and a successful approach to its management has not been well reported here. We present a case of a 13-year-old boy with Prader-Willi Syndrome with prom...
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| Format: | Article |
| Language: | English |
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2020
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| Online Access: | http://irep.iium.edu.my/81233/ http://irep.iium.edu.my/81233/1/10A_Case_Of_Prader-Willi_Syndrome_With_Behavioural_Disturbances_A_Successful_Multidisciplinary_Management_Approach.pdf |
| _version_ | 1848789095183024128 |
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| author | Md Rosli, Najwa Hanim Md Tahir, Mohd Faiz |
| author_facet | Md Rosli, Najwa Hanim Md Tahir, Mohd Faiz |
| author_sort | Md Rosli, Najwa Hanim |
| building | IIUM Repository |
| collection | Online Access |
| description | Prader-Willi Syndrome (PWS) is a genetically determined neurodevelopmental disorder occurring in 1 in 15,000 births. PWS is a rare case in Malaysia and a successful approach to its management has not been well reported here. We present a case of a 13-year-old boy with Prader-Willi Syndrome with prominent behavioural disturbances characterised by temper tantrums, compulsive food intake, stubbornness, stealing and impulsivity further complicated by underlying morbid obesity, poorly controlled type 2 diabetes mellitus, hypertension, dyslipidaemia, obstructive sleep apnoea syndrome and intellectual disability. Multidisciplinary approach involving child and adolescent psychiatrist, occupational therapist, counsellor, family therapist, endocrinologist and dietician has shown to improve the patient’s weight, glucose and blood pressure control and most importantly the behavioural disturbances. |
| first_indexed | 2025-11-14T17:51:16Z |
| format | Article |
| id | iium-81233 |
| institution | International Islamic University Malaysia |
| institution_category | Local University |
| language | English |
| last_indexed | 2025-11-14T17:51:16Z |
| publishDate | 2020 |
| recordtype | eprints |
| repository_type | Digital Repository |
| spelling | iium-812332020-07-06T08:22:35Z http://irep.iium.edu.my/81233/ A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach Md Rosli, Najwa Hanim Md Tahir, Mohd Faiz R Medicine (General) Prader-Willi Syndrome (PWS) is a genetically determined neurodevelopmental disorder occurring in 1 in 15,000 births. PWS is a rare case in Malaysia and a successful approach to its management has not been well reported here. We present a case of a 13-year-old boy with Prader-Willi Syndrome with prominent behavioural disturbances characterised by temper tantrums, compulsive food intake, stubbornness, stealing and impulsivity further complicated by underlying morbid obesity, poorly controlled type 2 diabetes mellitus, hypertension, dyslipidaemia, obstructive sleep apnoea syndrome and intellectual disability. Multidisciplinary approach involving child and adolescent psychiatrist, occupational therapist, counsellor, family therapist, endocrinologist and dietician has shown to improve the patient’s weight, glucose and blood pressure control and most importantly the behavioural disturbances. 2020-06 Article PeerReviewed application/pdf en http://irep.iium.edu.my/81233/1/10A_Case_Of_Prader-Willi_Syndrome_With_Behavioural_Disturbances_A_Successful_Multidisciplinary_Management_Approach.pdf Md Rosli, Najwa Hanim and Md Tahir, Mohd Faiz (2020) A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach. Jurnal of Clinical and Health Sciences, 5 (1). pp. 83-86. E-ISSN 0127-984X http://jchs-medicine.uitm.edu.my |
| spellingShingle | R Medicine (General) Md Rosli, Najwa Hanim Md Tahir, Mohd Faiz A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach |
| title | A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach |
| title_full | A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach |
| title_fullStr | A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach |
| title_full_unstemmed | A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach |
| title_short | A case of Prader-Willi Syndrome with Behavioural Disturbances: a successful multidisciplinary management approach |
| title_sort | case of prader-willi syndrome with behavioural disturbances: a successful multidisciplinary management approach |
| topic | R Medicine (General) |
| url | http://irep.iium.edu.my/81233/ http://irep.iium.edu.my/81233/ http://irep.iium.edu.my/81233/1/10A_Case_Of_Prader-Willi_Syndrome_With_Behavioural_Disturbances_A_Successful_Multidisciplinary_Management_Approach.pdf |