Primary Pulmonary Hypertension
Primary pulmonary hypertension(PPH) is a rare disease. The annual incidence in the West is 1-2 cases per million population per year. A recent WHO symposium in 1998 has produced a consensus on classification, methods of screening, risk assessment and treatment. PPH is a diagnosis of exclusion after...
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| Format: | Article |
| Language: | English |
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Malaysian Medical Association
2000
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| Online Access: | http://irep.iium.edu.my/5876/ http://irep.iium.edu.my/5876/1/Primary_Pulmonary_Hypertension.pdf |
| _version_ | 1848776580218748928 |
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| author | Abdul Rani, Mohammed Fauzi |
| author_facet | Abdul Rani, Mohammed Fauzi |
| author_sort | Abdul Rani, Mohammed Fauzi |
| building | IIUM Repository |
| collection | Online Access |
| description | Primary pulmonary hypertension(PPH) is a rare disease. The annual incidence in the West is 1-2 cases per million population per year. A recent WHO symposium in 1998 has produced a consensus on classification, methods of screening, risk assessment and treatment. PPH is a diagnosis of exclusion after all other secondary causes of pulmonary hypertension are ruled out. Current treatment strategy involves acute vasodilator drug trial where positive responders are treated with high dose calcium channel blockers and anticoagulation. Those who do not show positive response may be commenced on intravenous prostacyclin. Surgical treatment is one option for patients with severe PPH or for symptomatic relief. Prognosis in general is very poor. |
| first_indexed | 2025-11-14T14:32:21Z |
| format | Article |
| id | iium-5876 |
| institution | International Islamic University Malaysia |
| institution_category | Local University |
| language | English |
| last_indexed | 2025-11-14T14:32:21Z |
| publishDate | 2000 |
| publisher | Malaysian Medical Association |
| recordtype | eprints |
| repository_type | Digital Repository |
| spelling | iium-58762013-06-26T00:21:27Z http://irep.iium.edu.my/5876/ Primary Pulmonary Hypertension Abdul Rani, Mohammed Fauzi R Medicine (General) Primary pulmonary hypertension(PPH) is a rare disease. The annual incidence in the West is 1-2 cases per million population per year. A recent WHO symposium in 1998 has produced a consensus on classification, methods of screening, risk assessment and treatment. PPH is a diagnosis of exclusion after all other secondary causes of pulmonary hypertension are ruled out. Current treatment strategy involves acute vasodilator drug trial where positive responders are treated with high dose calcium channel blockers and anticoagulation. Those who do not show positive response may be commenced on intravenous prostacyclin. Surgical treatment is one option for patients with severe PPH or for symptomatic relief. Prognosis in general is very poor. Malaysian Medical Association 2000-12-04 Article NonPeerReviewed application/pdf en http://irep.iium.edu.my/5876/1/Primary_Pulmonary_Hypertension.pdf Abdul Rani, Mohammed Fauzi (2000) Primary Pulmonary Hypertension. Medical Journal Malaysia, 55 (4). pp. 529-537. ISSN 0300-5283 http://www.e-mjm.org/2000/v55n4/Primary_Pulmonary_Hypertension.pdf http://www.e-mjm.org/2000/v55n4/Primary_Pulmonary_Hypertension.pdf |
| spellingShingle | R Medicine (General) Abdul Rani, Mohammed Fauzi Primary Pulmonary Hypertension |
| title | Primary Pulmonary Hypertension |
| title_full | Primary Pulmonary Hypertension |
| title_fullStr | Primary Pulmonary Hypertension |
| title_full_unstemmed | Primary Pulmonary Hypertension |
| title_short | Primary Pulmonary Hypertension |
| title_sort | primary pulmonary hypertension |
| topic | R Medicine (General) |
| url | http://irep.iium.edu.my/5876/ http://irep.iium.edu.my/5876/ http://irep.iium.edu.my/5876/ http://irep.iium.edu.my/5876/1/Primary_Pulmonary_Hypertension.pdf |