A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report
Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal prolife...
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| Format: | Article |
| Language: | English |
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University of Malaya Medical Centre
2006
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| Online Access: | http://irep.iium.edu.my/44330/ http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf |
| _version_ | 1848782592258605056 |
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| author | How, Soon Hin Sa'at@Yusof, Azlin Pang, Yong-Kek Liam, Chong-Kin |
| author_facet | How, Soon Hin Sa'at@Yusof, Azlin Pang, Yong-Kek Liam, Chong-Kin |
| author_sort | How, Soon Hin |
| building | IIUM Repository |
| collection | Online Access |
| description | Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that
of fat. |
| first_indexed | 2025-11-14T16:07:54Z |
| format | Article |
| id | iium-44330 |
| institution | International Islamic University Malaysia |
| institution_category | Local University |
| language | English |
| last_indexed | 2025-11-14T16:07:54Z |
| publishDate | 2006 |
| publisher | University of Malaya Medical Centre |
| recordtype | eprints |
| repository_type | Digital Repository |
| spelling | iium-443302015-08-21T01:40:20Z http://irep.iium.edu.my/44330/ A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report How, Soon Hin Sa'at@Yusof, Azlin Pang, Yong-Kek Liam, Chong-Kin R Medicine (General) Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat. University of Malaya Medical Centre 2006 Article PeerReviewed application/pdf en http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf How, Soon Hin and Sa'at@Yusof, Azlin and Pang, Yong-Kek and Liam, Chong-Kin (2006) A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report. Journal of Health and Translational Medicine, 6 (2). pp. 35-38. ISSN 2289-392X (O), 1823-7339 (P) http://jummec.um.edu.my/filebank/published_article/3326/How%20SH.pdf |
| spellingShingle | R Medicine (General) How, Soon Hin Sa'at@Yusof, Azlin Pang, Yong-Kek Liam, Chong-Kin A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| title | A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| title_full | A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| title_fullStr | A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| title_full_unstemmed | A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| title_short | A case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| title_sort | case of lymphangioleiomyomatosis with multiple angiomyolipomas in the kidneys: a case report |
| topic | R Medicine (General) |
| url | http://irep.iium.edu.my/44330/ http://irep.iium.edu.my/44330/ http://irep.iium.edu.my/44330/1/case_of_lymphangioleiomyomatosis.pdf |