USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7

© 2017 The Authors. Published under the terms of the CC BY 4.0 license The amplitude of transforming growth factor-ß (TGF-ß) signal is tightly regulated to ensure appropriate physiological responses. As part of negative feedback loop SMAD7, a direct transcriptional target of downstream TGF-ß signali...

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Main Authors: Kit Leng Lui, S., Iyengar, P., Jaynes, P., Isa, Z., Pang, B., Tan, T., Eichhorn, Pieter
Format: Journal Article
Published: Wiley-Blackwell Publishing Ltd. 2017
Online Access:http://hdl.handle.net/20.500.11937/71914
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author Kit Leng Lui, S.
Iyengar, P.
Jaynes, P.
Isa, Z.
Pang, B.
Tan, T.
Eichhorn, Pieter
author_facet Kit Leng Lui, S.
Iyengar, P.
Jaynes, P.
Isa, Z.
Pang, B.
Tan, T.
Eichhorn, Pieter
author_sort Kit Leng Lui, S.
building Curtin Institutional Repository
collection Online Access
description © 2017 The Authors. Published under the terms of the CC BY 4.0 license The amplitude of transforming growth factor-ß (TGF-ß) signal is tightly regulated to ensure appropriate physiological responses. As part of negative feedback loop SMAD7, a direct transcriptional target of downstream TGF-ß signaling acts as a scaffold to recruit the E3 ligase SMURF2 to target the TGF-ß receptor complex for ubiquitin-mediated degradation. Here, we identify the deubiquitinating enzyme USP26 as a novel integral component of this negative feedback loop. We demonstrate that TGF-ß rapidly enhances the expression of USP26 and reinforces SMAD7 stability by limiting the ubiquitin-mediated turnover of SMAD7. Conversely, knockdown of USP26 rapidly degrades SMAD7 resulting in TGF-ß receptor stabilization and enhanced levels of p-SMAD2. Clinically, loss of USP26 correlates with high TGF-ß activity and confers poor prognosis in glioblastoma. Our data identify USP26 as a novel negative regulator of the TGF-ß pathway and suggest that loss of USP26 expression may be an important factor in glioblastoma pathogenesis.
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institution Curtin University Malaysia
institution_category Local University
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publishDate 2017
publisher Wiley-Blackwell Publishing Ltd.
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spelling curtin-20.500.11937-719142020-06-01T23:46:48Z USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7 Kit Leng Lui, S. Iyengar, P. Jaynes, P. Isa, Z. Pang, B. Tan, T. Eichhorn, Pieter © 2017 The Authors. Published under the terms of the CC BY 4.0 license The amplitude of transforming growth factor-ß (TGF-ß) signal is tightly regulated to ensure appropriate physiological responses. As part of negative feedback loop SMAD7, a direct transcriptional target of downstream TGF-ß signaling acts as a scaffold to recruit the E3 ligase SMURF2 to target the TGF-ß receptor complex for ubiquitin-mediated degradation. Here, we identify the deubiquitinating enzyme USP26 as a novel integral component of this negative feedback loop. We demonstrate that TGF-ß rapidly enhances the expression of USP26 and reinforces SMAD7 stability by limiting the ubiquitin-mediated turnover of SMAD7. Conversely, knockdown of USP26 rapidly degrades SMAD7 resulting in TGF-ß receptor stabilization and enhanced levels of p-SMAD2. Clinically, loss of USP26 correlates with high TGF-ß activity and confers poor prognosis in glioblastoma. Our data identify USP26 as a novel negative regulator of the TGF-ß pathway and suggest that loss of USP26 expression may be an important factor in glioblastoma pathogenesis. 2017 Journal Article http://hdl.handle.net/20.500.11937/71914 10.15252/embr.201643270 Wiley-Blackwell Publishing Ltd. restricted
spellingShingle Kit Leng Lui, S.
Iyengar, P.
Jaynes, P.
Isa, Z.
Pang, B.
Tan, T.
Eichhorn, Pieter
USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7
title USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7
title_full USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7
title_fullStr USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7
title_full_unstemmed USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7
title_short USP26 regulates TGF-ß signaling by deubiquitinating and stabilizing SMAD7
title_sort usp26 regulates tgf-ß signaling by deubiquitinating and stabilizing smad7
url http://hdl.handle.net/20.500.11937/71914