Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia

ß- thalassaemia is a disorder of globin gene synthesis resulting in reduced or absent production of the ß-globin chain in red blood cells. In this study, haematopoietic stem cells were isolated from the peripheral blood of six transfusion dependent ß-thalassaemia patients and six healthy controls. F...

Full description

Bibliographic Details
Main Authors: Forster, L., McCooke, J., Bellgard, M., Joske, D., Finlayson, J., Ghassemifar, Reza
Format: Journal Article
Published: Blackwell Publishing Ltd 2015
Online Access:http://hdl.handle.net/20.500.11937/36224
_version_ 1848754708847525888
author Forster, L.
McCooke, J.
Bellgard, M.
Joske, D.
Finlayson, J.
Ghassemifar, Reza
author_facet Forster, L.
McCooke, J.
Bellgard, M.
Joske, D.
Finlayson, J.
Ghassemifar, Reza
author_sort Forster, L.
building Curtin Institutional Repository
collection Online Access
description ß- thalassaemia is a disorder of globin gene synthesis resulting in reduced or absent production of the ß-globin chain in red blood cells. In this study, haematopoietic stem cells were isolated from the peripheral blood of six transfusion dependent ß-thalassaemia patients and six healthy controls. Following 7 and 14 d in culture, early- and late- erythroblasts were isolated and purified. No morphological difference in maturation was observed following 7 d in culture, while a delayed maturation was observed in the patient group after 14 d. Following RNA isolation and linear amplification, gene expression analyses were performed using microarray technology. The generated data were analysed by two methods: the BRB-ArrayTools platform and the Bioconductor platform using bead level data. Following 7 d culture, there was no difference in gene expression between the control and patient groups. Following 14 d culture, 384 differentially expressed genes were identified by either analysis. A subset of 90 genes was selected and the results were confirmed by Quantitative-Real-Time-polymerase chain reaction. Pathways shown to be significantly altered in the patient group include apoptosis, MAPKinase and the nuclear factor-KB pathway.
first_indexed 2025-11-14T08:44:43Z
format Journal Article
id curtin-20.500.11937-36224
institution Curtin University Malaysia
institution_category Local University
last_indexed 2025-11-14T08:44:43Z
publishDate 2015
publisher Blackwell Publishing Ltd
recordtype eprints
repository_type Digital Repository
spelling curtin-20.500.11937-362242018-06-20T03:15:26Z Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia Forster, L. McCooke, J. Bellgard, M. Joske, D. Finlayson, J. Ghassemifar, Reza ß- thalassaemia is a disorder of globin gene synthesis resulting in reduced or absent production of the ß-globin chain in red blood cells. In this study, haematopoietic stem cells were isolated from the peripheral blood of six transfusion dependent ß-thalassaemia patients and six healthy controls. Following 7 and 14 d in culture, early- and late- erythroblasts were isolated and purified. No morphological difference in maturation was observed following 7 d in culture, while a delayed maturation was observed in the patient group after 14 d. Following RNA isolation and linear amplification, gene expression analyses were performed using microarray technology. The generated data were analysed by two methods: the BRB-ArrayTools platform and the Bioconductor platform using bead level data. Following 7 d culture, there was no difference in gene expression between the control and patient groups. Following 14 d culture, 384 differentially expressed genes were identified by either analysis. A subset of 90 genes was selected and the results were confirmed by Quantitative-Real-Time-polymerase chain reaction. Pathways shown to be significantly altered in the patient group include apoptosis, MAPKinase and the nuclear factor-KB pathway. 2015 Journal Article http://hdl.handle.net/20.500.11937/36224 10.1111/bjh.13432 Blackwell Publishing Ltd restricted
spellingShingle Forster, L.
McCooke, J.
Bellgard, M.
Joske, D.
Finlayson, J.
Ghassemifar, Reza
Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
title Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
title_full Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
title_fullStr Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
title_full_unstemmed Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
title_short Differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
title_sort differential gene expression analysis in early and late erythroid progenitor cells in ß-thalassaemia
url http://hdl.handle.net/20.500.11937/36224