Oxidative stress and pathology in muscular dystrophies: focus on protein thiol oxidation and dysferlinopathies

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Oxidative stress and pathology in muscular dystrophies: focus on protein thiol oxidation and dysferlinopathies

The muscular dystrophies comprise more than 30 clinical disorders that are characterized by progressive skeletal muscle wasting and degeneration. Although the genetic basis for many of these disorders has been identified, the exact mechanism for pathogenesis generally remains unknown. It is consider...

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Bibliographic Details
Main Authors:	Terrill, J., Radley-Crabb, Hannah, Iwasaki, T., Lemckert, F., Arthur, P., Grounds, M.
Format:	Journal Article
Published:	Blackwell Publishing 2013
Subjects:	N-acetylcysteine Dysferlinopathies antioxidants reactive oxygen species Duchenne muscular dystrophy dystropathology muscle necrosis skeletal muscle protein thiol oxidation oxidative stress
Online Access:	http://hdl.handle.net/20.500.11937/33827

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