Role of international registries in enhancing the care of familial hypercholesterolaemia

Familial hypercholesterolaemia (FH) is a relatively common genetic disorder associated with high risk of coronary heart disease that is preventable by early diagnosis and treatment. In a previous article, we reviewed the evidence for clinical management, models of care and health economic evaluation...

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Main Authors: Hammond, E., Watts, G., Rubinstein, Y., Farid, W., Livingston, M., Knowles, J., Lochmuller, H., Bellgard, M., Dawkins, Hugh
Format: Journal Article
Published: Wiley-Blackwell Publishing Asia 2013
Subjects:
Online Access:http://hdl.handle.net/20.500.11937/32500
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author Hammond, E.
Watts, G.
Rubinstein, Y.
Farid, W.
Livingston, M.
Knowles, J.
Lochmuller, H.
Bellgard, M.
Dawkins, Hugh
author_facet Hammond, E.
Watts, G.
Rubinstein, Y.
Farid, W.
Livingston, M.
Knowles, J.
Lochmuller, H.
Bellgard, M.
Dawkins, Hugh
author_sort Hammond, E.
building Curtin Institutional Repository
collection Online Access
description Familial hypercholesterolaemia (FH) is a relatively common genetic disorder associated with high risk of coronary heart disease that is preventable by early diagnosis and treatment. In a previous article, we reviewed the evidence for clinical management, models of care and health economic evaluations. The present commentary emphasises that collective action is needed to strengthen our approaches to evidence-based care, including better diagnosis and access to effective therapies. We detail how contemporary innovations in inter-operable, web-based, open-source and secure registries can provide the supporting infrastructure to: (i) address a current gap in the flow of data for measuring the quality of healthcare; (ii) support basic research through provision of high-quality, de-identified aggregate data; (iii) enable equitable access to clinical trials; and (iv) support efforts to disseminate evidence for best practice and information for care services. We describe how these aspects of enabling infrastructure will be incorporated into the development of a National FH Registry for Australasia, and proffer that a coordinated response to FH would be enhanced through a global network of inter-operable registries.
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spelling curtin-20.500.11937-325002018-03-29T09:08:13Z Role of international registries in enhancing the care of familial hypercholesterolaemia Hammond, E. Watts, G. Rubinstein, Y. Farid, W. Livingston, M. Knowles, J. Lochmuller, H. Bellgard, M. Dawkins, Hugh model of care familial hypercholesterolaemia disease registry web-based open-source health economic evaluations Familial hypercholesterolaemia (FH) is a relatively common genetic disorder associated with high risk of coronary heart disease that is preventable by early diagnosis and treatment. In a previous article, we reviewed the evidence for clinical management, models of care and health economic evaluations. The present commentary emphasises that collective action is needed to strengthen our approaches to evidence-based care, including better diagnosis and access to effective therapies. We detail how contemporary innovations in inter-operable, web-based, open-source and secure registries can provide the supporting infrastructure to: (i) address a current gap in the flow of data for measuring the quality of healthcare; (ii) support basic research through provision of high-quality, de-identified aggregate data; (iii) enable equitable access to clinical trials; and (iv) support efforts to disseminate evidence for best practice and information for care services. We describe how these aspects of enabling infrastructure will be incorporated into the development of a National FH Registry for Australasia, and proffer that a coordinated response to FH would be enhanced through a global network of inter-operable registries. 2013 Journal Article http://hdl.handle.net/20.500.11937/32500 10.1111/1744-1609.12023 Wiley-Blackwell Publishing Asia restricted
spellingShingle model of care
familial hypercholesterolaemia
disease registry
web-based
open-source
health economic evaluations
Hammond, E.
Watts, G.
Rubinstein, Y.
Farid, W.
Livingston, M.
Knowles, J.
Lochmuller, H.
Bellgard, M.
Dawkins, Hugh
Role of international registries in enhancing the care of familial hypercholesterolaemia
title Role of international registries in enhancing the care of familial hypercholesterolaemia
title_full Role of international registries in enhancing the care of familial hypercholesterolaemia
title_fullStr Role of international registries in enhancing the care of familial hypercholesterolaemia
title_full_unstemmed Role of international registries in enhancing the care of familial hypercholesterolaemia
title_short Role of international registries in enhancing the care of familial hypercholesterolaemia
title_sort role of international registries in enhancing the care of familial hypercholesterolaemia
topic model of care
familial hypercholesterolaemia
disease registry
web-based
open-source
health economic evaluations
url http://hdl.handle.net/20.500.11937/32500