Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders

Background: Rett syndrome is a pervasive neurological disorder with impaired gait as one criterion. This study investigated the capacity of three accelerometer-type devices to measure walking activity in Rett syndrome. Methods: Twenty-six participants (mean 18 years, SD 8) wore an Actigraph, ActivPA...

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Main Authors: Downs, Jennepher, Leonard, H., Jacoby, P., Brisco, L., Baikie, G., Hill, Kylie
Format: Journal Article
Published: Taylor and Francis Ltd 2015
Online Access:http://hdl.handle.net/20.500.11937/28124
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author Downs, Jennepher
Leonard, H.
Jacoby, P.
Brisco, L.
Baikie, G.
Hill, Kylie
author_facet Downs, Jennepher
Leonard, H.
Jacoby, P.
Brisco, L.
Baikie, G.
Hill, Kylie
author_sort Downs, Jennepher
building Curtin Institutional Repository
collection Online Access
description Background: Rett syndrome is a pervasive neurological disorder with impaired gait as one criterion. This study investigated the capacity of three accelerometer-type devices to measure walking activity in Rett syndrome. Methods: Twenty-six participants (mean 18 years, SD 8) wore an Actigraph, ActivPAL and StepWatch Activity Monitor (SAM) during a video-taped session of activities. Agreement was determined between step-counts derived from each accelerometer and observation. Repeatability of SAM-derived step counts was determined using pairs of one-minute epochs during which the same participant was observed to walk with the same cadence. Results: The mean difference (limit of agreement) for the Actigraph, ActivPAL and SAM were −41 (SD 33), −16 (SD 21) and −1 (SD 16) steps/min, respectively. Agreement was influenced by a device/cadence interaction (p < 0.001) with greater under-recording at higher cadences. For SAM data, repeatability of step-count pairs was excellent (intraclass correlation coefficient 0.91, 95% CI 0.79–0.96). The standard error of measurement was 6 steps/min and we would be 95% confident that a change ≥17 steps/min would be greater than within-subject measurement error. Conclusions: The capacity of the SAM to measure physical activity in Rett syndrome allows focus on participation-based activities in clinical practice and clinical trials.
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spelling curtin-20.500.11937-281242017-09-13T15:14:32Z Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders Downs, Jennepher Leonard, H. Jacoby, P. Brisco, L. Baikie, G. Hill, Kylie Background: Rett syndrome is a pervasive neurological disorder with impaired gait as one criterion. This study investigated the capacity of three accelerometer-type devices to measure walking activity in Rett syndrome. Methods: Twenty-six participants (mean 18 years, SD 8) wore an Actigraph, ActivPAL and StepWatch Activity Monitor (SAM) during a video-taped session of activities. Agreement was determined between step-counts derived from each accelerometer and observation. Repeatability of SAM-derived step counts was determined using pairs of one-minute epochs during which the same participant was observed to walk with the same cadence. Results: The mean difference (limit of agreement) for the Actigraph, ActivPAL and SAM were −41 (SD 33), −16 (SD 21) and −1 (SD 16) steps/min, respectively. Agreement was influenced by a device/cadence interaction (p < 0.001) with greater under-recording at higher cadences. For SAM data, repeatability of step-count pairs was excellent (intraclass correlation coefficient 0.91, 95% CI 0.79–0.96). The standard error of measurement was 6 steps/min and we would be 95% confident that a change ≥17 steps/min would be greater than within-subject measurement error. Conclusions: The capacity of the SAM to measure physical activity in Rett syndrome allows focus on participation-based activities in clinical practice and clinical trials. 2015 Journal Article http://hdl.handle.net/20.500.11937/28124 10.3109/09638288.2014.993436 Taylor and Francis Ltd fulltext
spellingShingle Downs, Jennepher
Leonard, H.
Jacoby, P.
Brisco, L.
Baikie, G.
Hill, Kylie
Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
title Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
title_full Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
title_fullStr Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
title_full_unstemmed Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
title_short Rett syndrome: Establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
title_sort rett syndrome: establishing a novel outcome measure for walking activity in an era of clinical trials for rare disorders
url http://hdl.handle.net/20.500.11937/28124