Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome
Background: Scoliosis is a common orthopaedic complication of Rett syndrome, and surgery is commonly used to reduce asymmetry in cases with severe scoliosis.Methods: Data from questionnaires administered to caregivers biennially from 2000 to 2006 were used to describe functional skill levels in subj...
| Main Authors: | , , , , , |
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| Format: | Journal Article |
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Lippincott Williams & Wilkins
2009
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| Online Access: | http://hdl.handle.net/20.500.11937/2651 |
| _version_ | 1848744012258738176 |
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| author | Downs, Jennepher Young, D. De Klerk, N. Bebbington, A. Baikie, G. Leonard, H. |
| author_facet | Downs, Jennepher Young, D. De Klerk, N. Bebbington, A. Baikie, G. Leonard, H. |
| author_sort | Downs, Jennepher |
| building | Curtin Institutional Repository |
| collection | Online Access |
| description | Background: Scoliosis is a common orthopaedic complication of Rett syndrome, and surgery is commonly used to reduce asymmetry in cases with severe scoliosis.Methods: Data from questionnaires administered to caregivers biennially from 2000 to 2006 were used to describe functional skill levels in subjects with Rett syndrome, and within-subject change in16 subjects with scoliosis surgery were compared with within-subject change in 186 pairs of data from 86 subjects with conservatively managed scoliosis. Postsurgical assessment was conducted after amean of 17.8 months.Results: Surgery was associated with improved activities of daily living as measured by the WeeFIM for subjects who were wheelchair bound (P = 0.05). Mobility levels, social interaction, communicationskills, and the frequency of daytime napping remained similar for the group as a whole.Conclusions: Improvements in activities of daily living are likely to represent an increase in the quality of life for subjects and caregivers and were mainly found in subjects who were wheelchair bound,indicating that those who were more severely affected were able to benefit from this intervention.Level of Evidence: Therapeutic study: level III |
| first_indexed | 2025-11-14T05:54:42Z |
| format | Journal Article |
| id | curtin-20.500.11937-2651 |
| institution | Curtin University Malaysia |
| institution_category | Local University |
| last_indexed | 2025-11-14T05:54:42Z |
| publishDate | 2009 |
| publisher | Lippincott Williams & Wilkins |
| recordtype | eprints |
| repository_type | Digital Repository |
| spelling | curtin-20.500.11937-26512017-09-13T14:32:14Z Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome Downs, Jennepher Young, D. De Klerk, N. Bebbington, A. Baikie, G. Leonard, H. scoliosis spinal fusion Rett syndrome neuromuscular scoliosis function Background: Scoliosis is a common orthopaedic complication of Rett syndrome, and surgery is commonly used to reduce asymmetry in cases with severe scoliosis.Methods: Data from questionnaires administered to caregivers biennially from 2000 to 2006 were used to describe functional skill levels in subjects with Rett syndrome, and within-subject change in16 subjects with scoliosis surgery were compared with within-subject change in 186 pairs of data from 86 subjects with conservatively managed scoliosis. Postsurgical assessment was conducted after amean of 17.8 months.Results: Surgery was associated with improved activities of daily living as measured by the WeeFIM for subjects who were wheelchair bound (P = 0.05). Mobility levels, social interaction, communicationskills, and the frequency of daytime napping remained similar for the group as a whole.Conclusions: Improvements in activities of daily living are likely to represent an increase in the quality of life for subjects and caregivers and were mainly found in subjects who were wheelchair bound,indicating that those who were more severely affected were able to benefit from this intervention.Level of Evidence: Therapeutic study: level III 2009 Journal Article http://hdl.handle.net/20.500.11937/2651 10.1097/BPO.0b013e3181a53b41 Lippincott Williams & Wilkins restricted |
| spellingShingle | scoliosis spinal fusion Rett syndrome neuromuscular scoliosis function Downs, Jennepher Young, D. De Klerk, N. Bebbington, A. Baikie, G. Leonard, H. Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome |
| title | Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome |
| title_full | Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome |
| title_fullStr | Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome |
| title_full_unstemmed | Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome |
| title_short | Impact of scoliosis surgery on activites of daily living in females with Rett Syndrome |
| title_sort | impact of scoliosis surgery on activites of daily living in females with rett syndrome |
| topic | scoliosis spinal fusion Rett syndrome neuromuscular scoliosis function |
| url | http://hdl.handle.net/20.500.11937/2651 |